X-LINKED INHIBITOR OF APOPTOSIS (XIAP) DEFICIENCY PRESENTING AS HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS TRIGGERED BY DRUG ALLERGY

X-Linked Inhibitor of Apoptosis (XIAP) deficiency presenting as hemophagocytic lymphohistiocytosis triggered by drug allergy

X-linked inhibitor of apoptosis (XIAP) deficiency is a primary immunodeficiency associated with recurrent hemophagocytic lymphohistiocytosis (HLH) episodes.The clinical phenotypes of XIAP deficiency vary, ranging from splenomegaly to life-threatening inflammation.We report a case of XIAP deficiency with unusual late-onset HLH presentation likely tr

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Understanding the reminiscence bump: A systematic review.

One of the most consistently observed phenomena in autobiographical memory research is the reminiscence bump: a tendency for middle-aged and elderly people to access more personal memories from approximately 10-30 years of age.This systematic review (PROSPERO 2017:CRD42017076695) aimed to synthesize peer-reviewed literature pertaining to the remini

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